McArdle disease: what do neurologists need to know?
A Lucia, G Nogales-Gadea, M Pérez… - Nature clinical practice …, 2008 - nature.com
McArdle disease (also known as glycogen storage disease type V) is a pure myopathy
caused by an inherited deficit of myophosphorylase, the skeletal muscle isoform of the …
caused by an inherited deficit of myophosphorylase, the skeletal muscle isoform of the …
Core-shell particles lead the way to renewing high-performance liquid chromatography
In this review, we present the latest highlights and trends in the use of core-shell particles as
stationary phases in columns for liquid chromatography (LC). These highly homogeneous …
stationary phases in columns for liquid chromatography (LC). These highly homogeneous …
Mitochondrial respiratory chain dysfunction: implications in neurodegeneration
M Morán, D Moreno-Lastres, L Marín-Buera… - Free Radical Biology …, 2012 - Elsevier
For decades mitochondria have been considered static round-shaped organelles in charge
of energy production. In contrast, they are highly dynamic cellular components that undergo …
of energy production. In contrast, they are highly dynamic cellular components that undergo …
Influence of inoculum–substrate ratio on the anaerobic digestion of sunflower oil cake in batch mode: process stability and kinetic evaluation
A study of the anaerobic digestion of the solid waste generated in the extraction process of
sunflower oil (sunflower oil cake, SuOC) was conducted at mesophilic temperature (35° C) …
sunflower oil (sunflower oil cake, SuOC) was conducted at mesophilic temperature (35° C) …
Biomethanization of orange peel waste
Recent research has demonstrated that orange peel waste is a potentially valuable resource
that can be developed into high value products such as methane. Following a pre-treatment …
that can be developed into high value products such as methane. Following a pre-treatment …
[PDF][PDF] Mitochondrial complex I plays an essential role in human respirasome assembly
D Moreno-Lastres, F Fontanesi, I García-Consuegra… - Cell metabolism, 2012 - cell.com
The biogenesis and function of the mitochondrial respiratory chain (RC) involve the
organization of RC enzyme complexes in supercomplexes or respirasomes through an …
organization of RC enzyme complexes in supercomplexes or respirasomes through an …
Mitochondrial respiratory activity is altered in osteoarthritic human articular chondrocytes
E Maneiro, MA Martín, MC de Andres… - Arthritis & …, 2003 - Wiley Online Library
Objective Osteoarthritis (OA) is a degenerative rheumatic disease that is associated with
extracellular matrix degradation and chondrocyte apoptosis in the articular cartilage. The …
extracellular matrix degradation and chondrocyte apoptosis in the articular cartilage. The …
Impact of ammonia and sulphate concentration on thermophilic anaerobic digestion
The effect of increasing concentrations of ammonia and sulphate on thermophilic anaerobic
digestion (52° C) was studied at laboratory-scale. The substrate consisted of a synthetic …
digestion (52° C) was studied at laboratory-scale. The substrate consisted of a synthetic …
Quercetin modulates Nrf2 and glutathione-related defenses in HepG2 cells: Involvement of p38
AB Granado-Serrano, MA Martín, L Bravo… - Chemico-Biological …, 2012 - Elsevier
Dietary flavonoid quercetin has been suggested as a cancer chemopreventive agent, but the
mechanisms of action remain unclear. This study investigated the influence of quercetin on …
mechanisms of action remain unclear. This study investigated the influence of quercetin on …
Complex I defect in muscle from patients with Huntington's disease
We found a variable defect of complex I of the mitochondrial respiratory chain, ranging in
severity from 25% to 63% of control values, in muscle of patients with Huntington's disease …
severity from 25% to 63% of control values, in muscle of patients with Huntington's disease …